Tag: what is Sodium phenylbutyrate

Pheburane – Sodium phenylbutyrate uses, dose and side effects

PHEBURANE contains the active substance sodium phenylbutyrate which is used to treat patients of all ages with urea metabolic disorders. These rare diseases are due to a deficiency of certain liver enzymes that are necessary to excrete residual nitrogen in the form of ammonia.

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Ammonaps – Sodium phenylbutyrate uses, dose and side effects

AMMONAPS is prescribed to patients with urea metabolic disorders. Patients suffering from these unusual disorders are deficient in certain liver enzymes and therefore cannot excrete nitrogen residues. Nitrogen is a building block in protein and therefore nitrogen accumulates in the body when you have eaten protein. Nitrogen residues in the form of ammonia are especially toxic to the brain and in severe cases lead to decreased consciousness and coma.

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